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Know the symptoms, diagnosis and treatment of Lymphangiomatosis

  • Posted on- Aug 31, 2015
  • 371 Views

Lymphangiomatosis is an uncommon health condition believed to be congenital can probably affect any part of the body. It is a medical condition of the lymphatic system. Lymphangiomatosis normally does not affect the central nervous system as the lymphatic system is not connected to it but it can definitely affect other vital organs of the body like heart, lungs, kidney, liver etc.

How does lymphangiomatosis affect the body?

Lymphangiomatosis can originate in just one part of body and gradually spread around various parts. It is very difficult to predict how the disease will affect from person to person. Lymphangiomatosis assists quick growth of tumours if they are present in any part of the body these tumours are usually benign but these tumours affect the normal functioning of the body. Following are some parts of the body which are usually affected by Lymphangiomatosis:

  • Lungs
  • Heart
  • The musculoskeletal system
  • Spleen
  • Abdomen
  • Pericardium
  • Kidneys
  • Liver

Individuals susceptible to Lymphangiomatosis

Lymphangiomatosis can affect anyone regardless of sex, age or race. Infants and young children are most susceptible to this disease. A diagnosis of Lymphangiomatosis is usually confirmed by the time an affected individual turns 20 years of age. Lymphangiomatosis is a rare condition and it is difficult to pinpoint as to who will be at definite risk for development of the disease.

What are the symptoms of Lymphangiomatosis?

A person suffering from lymphangiomatosis will have a range of symptoms depending on what part of the body or which organ system is affected by it and also the seriousness of the condition. Some of the signs and symptoms of lymphangiomatosis affecting the lungs are:

How is lymphangiomatosis diagnosed?

In order to perfectly diagnose lymphangiomatosis, several medical professionals will have to work in coordination as this disease affects multiple organ systems at one time and causing different symptoms. Some of the tests conducted are:
  • Radiological studies like X-rays, MRI and CT scans of the organ system depending on the symptoms to look at their functioning.
  • A biopsy of the organ may also be taken for confirmatory diagnosis.

Available treatment options for lymphangiomatosis

The treatment of lymphangiomatosis depends on the part of the body involved and the symptoms experienced by the patient. The objective of the treatment is to reduce symptoms and minimise pain. Some of the treatment methods adopted when lymphangiomatosis affects lungs are:
  • Drainage of fluid from lungs
  • Removing the lining of the chest cavity surgically
  • Medications to reduce pain and inflammation
  • Radiation to shrink tumours
  • Change in diet to include low fat and high protein
  • Lung transplantation, which may be the last option